Test Code TPIC Triosephosphate Isomerase Enzyme Activity, Blood
Reporting Name
Triosephosphate Isomerase, BPerforming Laboratory
Mayo Clinic Laboratories in RochesterUseful For
Evaluating individuals with chronic nonspherocytic hemolytic anemia
Evaluating individuals with early onset neurologic impairment
Genetic counseling for families with triosephosphate isomerase deficiency
Method Name
Only available as part of a profile. For more information see:
-HAEV1 / Hemolytic Anemia Evaluation, Blood
-EEEV1 / Red Blood Cell (RBC) Enzyme Evaluation, Blood
Kinetic Spectrophotometry
Specimen Required
Only available as part of a profile. For more information see:
-HAEV1 / Hemolytic Anemia Evaluation, Blood
-EEEV1 / Red Blood Cell (RBC) Enzyme Evaluation, Blood
Specimen Type
Whole Blood ACD-BSpecimen Minimum Volume
1 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Whole Blood ACD-B | Refrigerated | 20 days |
Reject Due To
Gross hemolysis | Reject |
Reference Values
Only available as part of a profile. For more information see:
-HAEV1 / Hemolytic Anemia Evaluation, Blood
-EEEV1 / Red Blood Cell (RBC) Enzyme Evaluation, Blood
≥12 months of age: 1033-1363 U/g Hb
Reference values have not been established for patients who are younger than 12 months of age.
Interpretation
Clinically significant hemolytic anemias due to triosephosphate isomerase deficiency are associated with activity levels less than 30% of mean normal. Heterozygotes usually show approximately 50% of mean normal activity and are clinically unaffected.
Day(s) Performed
Weekly, Varies
Report Available
5 daysTest Classification
This test was developed and its performance characteristics determined by Mayo Clinic in a manner consistent with CLIA requirements. It has not been cleared or approved by the US Food and Drug Administration.CPT Code Information
82657
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
TPIC | Triosephosphate Isomerase, B | 44054-5 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
TPICL | Triosephosphate Isomerase, B | 44054-5 |